Retroperitoneal Malignant Schwannoma Associated with Von Recklinghausen Disease

Hye Won Lee1, Hee Chung Sohn1, Ji Sung Kim1, Soon Nam Lee1, Eung Bum Park2, Hye Soo Ku3, Ok Kyung Kim3

Copyright ⓒ 1990. Ewha Womans University School of Medicine. This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Published Online: Jul 24, 2015

Abstract

Malignant schwannoma is a malignant neoplasm of nerve sheath cells. It develops in a solitary fashion or associated with Von Recklinghausen disease.

We experienced a malignant schwannoma in a 20-year old man with Von Recklinghausen disease. The lesion was gure, irregular, cystic and solid mass with septations in the right retroperitoneal region, inferior to the kidney. The histologic findings of retroperitoneal and pulmonary mass was compatible with malignant schwannoma. Incomplete excision due to infiltration to the adjacent tissue, radiotherapy and combined chemotherapy were performed.

We report a case of retroperitoneal malignant schwannoma associated with Von recklinghausen disease.